A nurse is caring for a school-age child who has cystic fibrosis.
Exhibits
A nurse is reviewing the child’s medical record. Which of the following medications should the nurse expect the provider to prescribe or reconcile from the child’s home medication list?
Select all that apply.
A. Water-soluble vitamins
B. Acetaminophen
C. Dornase alfa
D. Meperidine
E. Pancreatic lipase
The correct answer and Explanation is :
For a school-age child with cystic fibrosis, the nurse should expect the provider to prescribe or reconcile the following medications:
A. Water-soluble vitamins
C. Dornase alfa
E. Pancreatic lipase
Explanation:
- Water-soluble vitamins: Children with cystic fibrosis often have malabsorption issues due to pancreatic insufficiency. They are at risk for deficiencies in vitamins, especially the fat-soluble vitamins (A, D, E, and K). However, water-soluble vitamins (such as B vitamins and vitamin C) are also important for overall health. These vitamins may be supplemented to help meet the child’s nutritional needs.
- Dornase alfa: This medication is a recombinant human deoxyribonuclease I (rhDNase) that helps reduce mucus viscosity in the lungs, facilitating easier expectoration. This is a critical part of the management of cystic fibrosis, as thick mucus can lead to respiratory complications and infections. Dornase alfa is commonly prescribed to improve lung function in children with cystic fibrosis.
- Pancreatic lipase: Cystic fibrosis often results in pancreatic enzyme insufficiency, leading to difficulty in digesting fats and other nutrients. Pancreatic lipase supplements (such as pancrelipase) help break down dietary fats, aiding in nutrient absorption and preventing malnutrition. This is a cornerstone of management for children with cystic fibrosis.
Not Recommended:
- B. Acetaminophen: While it can be used for pain or fever, it is not specific to the management of cystic fibrosis.
- D. Meperidine: This opioid is generally avoided in children with cystic fibrosis due to its side effects and potential respiratory depression.
In summary, the key medications that align with the management of cystic fibrosis in children are water-soluble vitamins, dornase alfa, and pancreatic lipase, focusing on nutritional support and respiratory health.